Spinal Muscular Atrophy Type III
Conditions
Interventions
Experimental group: 1 child diagnosed with type III spinal muscular atrophy. The applied protocol was carried out for 6 months, comparing the results from the beginning with those after 3 months and t
C10.228.854.468.800
Sponsors
Universidade Paulista
Clinica ser especial- Centro de terapia neuromotora intensiva
Eligibility
Sex/Gender
Female
Inclusion criteria
Inclusion criteria: 1 Patient with type III SMA. Informed consent form (TCLE), term of free and informed consent (TALE) and term of use of duly signed image.
Exclusion criteria
Exclusion criteria: Loss to follow-up or appearance of other comorbidities that alter the results of the applied protocol was considered as an exclusion criterion.
Design outcomes
Primary
| Measure | Time frame |
|---|---|
| Develop a motor and cardiorespiratory physiotherapy protocol for patients with type III SMA. - Assess gains in respiratory muscle strength and lung expansion in patients with type III SMA. - Assess improvement in range of motion, strength and postural assessment in patients with type III SMA. | — |
Secondary
| Measure | Time frame |
|---|---|
| there are the data regarding the cardiorespiratory evaluation, in which an improvement in the 6MWT test was observed, and the initial was 90 meters and at the end was 106 meters, the peak expiratory flow had an increase of 210L/min to 240L/min, in the assessment of respiratory muscle strength was verified increase in MIP from -80cmH2O to -100cmH2O and MEP from 70cmH2O to 100cmH2 and an improvement in lung expansion with increasing coefficient of variation in thoracic cirtometry from 3.0cm to 4.5cm and reduction of 0.5cm of abdominal perimeter. | — |
Countries
Brazil
Contacts
Public ContactEduarda Carvalho
Outcome results
None listed