Cystic Fibrosis immotile cilia syndrome mucoviscoidosis / Primary ciliary dyskinesia
Conditions
Interventions
None listed
Sponsors
Academisch Medisch Centrum
Eligibility
Age
2 Years to 17 Years
Inclusion criteria
Inclusion criteria: Patients: children 0 - 17 years old with cystic fibrosis or primary ciliary dykinesia Healthy controls: children 0 - 17 years old without pulmonary, metabolic, or inflammatory diseases
Exclusion criteria
Exclusion criteria: Patients: metabolic, or inflammatory disorders Healthy controls: pulmonary, metabolic or inflammatory disease
Design outcomes
Primary
| Measure | Time frame |
|---|---|
| The primary outome of this study will be: - the discrimination between CF and PCD patients with and without pulmonary infections - the discrimination between CF, PCD and healthy controls | — |
Secondary
| Measure | Time frame |
|---|---|
| none | — |
Countries
Netherlands
Outcome results
None listed