Fibroelastosis
Conditions
Brief summary
This retrospective observational study will evaluate the outcomes of lung transplantation for a rare cause of interstitial lung disease called pleuroparenchymal fibroelastosis. Data will be collected from all transplantation center in France.
Interventions
Lung transplantation were performed for end-stage interstitial lung disease secondary to pleuroparenchymal fibroelastosis
Sponsors
Study design
Eligibility
Inclusion criteria
* Lung transplantation (any type) for pleuroparenchymal fibroelastosis * Histologically confirmed pleuroparenchymal fibroelastosis on the recipient lungs
Exclusion criteria
* All other interstitial lung disease than pleuroparenchymal fibroelastosis * Pleuroparenchymal fibroelastosis who didn't underwent lung transplantation
Design outcomes
Primary
| Measure | Time frame | Description |
|---|---|---|
| Post-operative mortality | Any death up to 90 days after lung transplantation | Any death after lung transplantation during the first 30 days or during the hospitalization following the lung transplantation (in-hospital mortality) |
Countries
France