Pulmonary Venous Stenosis, Sutureless Closure, Total Anomalous Pulmonary Venous Connection
Conditions
Keywords
TAPVC, Sutureless, Pulmonary venous stenosis
Brief summary
The purpose of this study is to assess the percentage of pulmonary venous stenosis after TAPVC repair with sutureless closure.
Detailed description
Parents of patients with TAPVC after repairing by sutureless technique will be informed about the study. If parents agree to participant in the study and sign the informed consent, the investigators will collect information of patients and echocardiography results at 1 month, 6 month, 12 month and 18 month after the operation.
Interventions
None listed
Sponsors
Children's Hospital 1
Study design
Observational model
CASE_ONLY
Time perspective
PROSPECTIVE
Eligibility
Sex/Gender
ALL
Age
No minimum to 15 Years
Inclusion criteria
* All patients with TAPVC operated with sutureless closure and be agreed to join this study by parents from 01/2019 to 06/2024.
Exclusion criteria
* TAPVC operated with sutureless closure have single ventricle, isomerism or heterotaxy, congenital pulmonary venous stenosis. * TAPVC enrolled to study but cannot the obtain the echocardiography at the time of 1 month, 6 month, 12 month and 18 month.
Design outcomes
Primary
| Measure | Time frame | Description |
|---|---|---|
| The percentage of pulmonary venous stenosis after reparing TAPVC with sutureless technique | The investigators assess the PVS at the time of 12 month after the operation. | The investigators calculate pulmonary venous score (PVS) based on the mean gradient through each pulmonary vein. Then we sum all the score of each pulmonary vein, range from 0 to 12, and classify to 4 levels. Score 0 if the mean gradient is less than 2mmHg, 1 if it is from 2 to 6,9mmHg, 2 if it is from 7 mmHg and above, and 3 if the vein is occluded. The degree of obstruction is classified as follow: none (0 to 1), mild (2 to 3), moderate (4 to 7), and severe (from 8 and above). |
| Early mortality (<30 days) | 30 days | Early mortality is defined when patients die within 30 days since the operation |
Secondary
| Measure | Time frame | Description |
|---|---|---|
| Late mortality (> 30 days) | The investigators assess mortality at the time of 18 month after the operation | Late mortality is defined when patients die beyond 30 day since the operation |
| The percentage of pulmonary venous stenosis after reparing TAPVC with sutureless technique | The investigators assess the PVS at the time of 6 month after the operation. | The investigator calculate pulmonary venous score (PVS) based on the mean gradient through each pulmonary vein. Then we sum all the score of each pulmonary vein, range from 0 to 12, and classify to 4 levels. Score 0 if the mean gradient is less than 2mmHg, 1 if it is from 2 to 6,9mmHg, 2 if it is from 7 mmHg and above, and 3 if the vein is occluded. The degree of obstruction is classified as follow: none (0 to 1), mild (2 to 3), moderate (4 to 7), and severe (from 8 and above). |
Countries
Vietnam
Contacts
Primary ContactThanh QL Dinh, MSC
Outcome results
None listed