Cystic Fibrosis, Bowel Obstruction, Distal Intestinal Obstruction Syndrome
Conditions
Brief summary
A case of a patient with cystic fibrosis with bowel obstruction due to a proximal intestinal obstruction syndrome (PIOS) is presented.This syndrome can be diagnosed with the DIOS definition, with the only distinction of a more proximal location in the gastrointestinal tract, such as the stomach, the duodenum, or the jejunum.
Detailed description
Distal Intestinal Obstruction Syndrome is a rare complication in cystic fibrosis patients characterized by the accumulation of viscid fecal material, combined with sticky mucous secretions located in the distal ileum, adhered to the intestinal wall. Only few cases have been reported in the literature.
Interventions
A diagnostic laparoscopy was performed where a dilated jejunum was encountered with impaction of fecal content. Surgery was converted to open surgery, where a longitudinal enterotomy of 5 cm after the transition zone was created, evacuating manually the fecal material with mucous secretion.
Sponsors
Tecnologico de Monterrey
Study design
Observational model
CASE_ONLY
Time perspective
RETROSPECTIVE
Eligibility
Sex/Gender
MALE
Healthy volunteers
No
Inclusion criteria
* Adult \>18 years * Cystic fibrosis * Bowel obstruction
Exclusion criteria
* Pediatric patient \<18 years * Unknown cause of bowel obstruction
Design outcomes
Primary
| Measure | Time frame | Description |
|---|---|---|
| Bowel obstruction in a patient with cystic fibrosis | 3-6 days | A 45 year old patient with cystic fibrosis presented with bowel obstruction. Image studies were performed, without identifying a specific cause of the bowel obstruction. The patient was transferred to surgery. |
Countries
Mexico
Outcome results
None listed