Pulmonary Hypertension in Lymphangioleiomyomatosis

Observational Study of Patients With Lymphangioleiomyomatosis and Pulmonary Hypertension

Status

Completed

Phases

Unknown

Study type

Observational

Source

ClinicalTrials.gov

Registry ID

NCT00960895

Acronym

LAM-PH

Enrollment

Registered

2009-08-18

Start date

2009-08-31

Completion date

2010-12-31

Last updated

2011-10-27

For informational purposes only — not medical advice. Sourced from public registries and may not reflect the latest updates. Terms

Conditions

Lymphangioleiomyomatosis, Pulmonary Hypertension

Keywords

Lymphangioleiomyomatosis, Pulmonary hypertension

Brief summary

This is a descriptive study of patients with Lymphangioleiomyomatosis and precapillary pulmonary hypertension.

Detailed description

Descriptive study of patients with Lymphangioleiomyomatosis and precapillary pulmonary hypertension This will include modality of diagnosis of lLymphangioleiomyomatosis, results of right-sided heart catheterization, and pulmonary function tests

Interventions

None listed

Study design

Observational model

CASE_ONLY

Time perspective

RETROSPECTIVE

Eligibility

Sex/Gender

FEMALE

Age

18 Years to No maximum

Healthy volunteers

Inclusion criteria

* Lymphangioleiomyomatosis (definite or probable), either sporadic or associated with tuberous sclerosis * Precapillary pulmonary hypertension, as defined by right-sided heart catheterization (mean pulmonary artery pressure higher than 25 mmHg, wedge capillary pulmonary pressure less than 15 mmHg, pulmonary vascular resistance higher than 3 Wood units)

Exclusion criteria

* Post capillary pulmonary hypertension * Other identifiable causes of pulmonary hypertension (ex: thromboembolic disease) * Not willing to participate

Countries

France

Outcome results