X- linked deafness revisited - longterm results following cochlear implantation

X- linked deafness revisited - longterm results following cochlear implantation - X- linked

Status

Active, not recruiting

Phases

Unknown

Study type

Observational

Source

DRKS

Registry ID

DRKS00016355

Enrollment

Registered

2019-01-07

Start date

2018-10-23

Completion date

Unknown

Last updated

2025-04-07

For informational purposes only — not medical advice. Sourced from public registries and may not reflect the latest updates. Terms

Conditions

deafness, cochlear implant, malformation rhinoliquorrhoea, facial paresis, facial stimulation, meningitis

Interventions

Group 1: X- linked patients with cochlear malformation, means missing lamina cribrosa between cochlear duct and internal auditory canal. Analysis of speech perception, longterm mapping data including

Eligibility

Sex/Gender

Male

Inclusion criteria

Inclusion criteria: X- linked patients with radiologically cochlear malformation and patients with normal cochlear morphology matched regarding sex, age, date of surgery, implant, side. Data has been collected between 1999 and 2018.

Exclusion criteria

Exclusion criteria: patients not fitting regarding matching with normal cochlear morphology and X- linked patients without cochlear implantation.

Design outcomes

Primary

Measure	Time frame
The aim of this study is to evaluate longterm speech perception, mapping data and electrophysiological data (ECAPs, impedances) of implanted X- linked patients. Furthermore, to compare the results to patients with normal cochlear morphology.	—

Secondary

Measure	Time frame
complications following implantation (rhinoliquorrhea and meningitis)	—

Countries

Germany

Contacts

Public ContactManuel Christoph Ketterer

Klinik für Hals- Nasen- Ohrenheilkunde

manuel.christoph.ketterer@uniklinik-freiburg.de0049076127041010

Outcome results

None listed

Source: DRKS (via WHO ICTRP) · Data processed: Feb 4, 2026