Congenital microvilli inclusion body disease
Conditions
Interventions
case series:None
Sponsors
The Seventh Medical Center of Chinese PLA General Hospital
Eligibility
Sex/Gender
All
Age
1 Years to 17 Years
Inclusion criteria
Inclusion criteria: Early onset, mainly intractable watery diarrhea, no relief after improving diet, increased fecal sodium ion content, blunting or disappearance of microvilli on enteroscopy, accumulation of secretory granules, microvillous inclusions were seen in epithelial cells, periodic acid Schiff staining and CD10 positivity.
Exclusion criteria
Exclusion criteria: None
Design outcomes
Primary
| Measure | Time frame |
|---|---|
| treatment effect;prognosis;diagnostic accuracy; | — |
Countries
China
Contacts
Public ContactXu Xuan
Seventh Medical Center of Chinese PLA General Hospital
Outcome results
None listed