Fibrosing mediastinitis
Conditions
Interventions
Sponsors
Eligibility
Inclusion criteria
Inclusion criteria: According to the pulmonary vascular CTA diagnosis of fibromediastinitis patients, specifically, chest enhanced CT showed that the mediastinal fibrous tissue hyperplasia wrapped and compressed the structure of the mediastinum and bronchial vessels.
Exclusion criteria
Exclusion criteria: 1. Patients with pulmonary hypertension from the first to the fourth categories; 2. Patients with lung tumor, mediastinal or hilar metastasis, suspected mediastinal necrotizing granulomatous lymphadenitis, systemic sclerosis, etc; 3. Patients with diffuse fibromediastinitis (patients with extrapulmonary diseases such as retroperitoneal fibrosis and sclerosing cholangitis, IgG4 positive patients).
Design outcomes
Primary
| Measure | Time frame |
|---|---|
| NT-proBNP;cTnT;Mean pulmonary artery pressure;Pulmonary artery systolic pressure;Cardiac output;6-minute walk distance;WHO functional class; | — |
Countries
China
Contacts
Gansu Provincial Hospital