Hemophagocytic lymphohistiocytosis
Conditions
Interventions
Sponsors
Eligibility
Inclusion criteria
Inclusion criteria: At the same time, the following three conditions are met: 1. Patients with hlh-2004 were diagnosed; 2. Both male and female, patients over the age of 16 years.
Exclusion criteria
Exclusion criteria: HScore < 90 points; Pathological mutations were found in currently known HLH-related pathogenic genes, such as PRFl, UNCl3D, STXll, STXBP2, Rab27a, LYST, SH2D1A, BIRC4, ITK, AP381, MAGTl, CD27, etc.
Design outcomes
Primary
| Measure | Time frame |
|---|---|
| overall survival;Short term survival; | — |
Countries
China
Contacts
The First Affiliated Hospital of Nanjing Medical University, Jiangsu Province Hospital